glucose-6-phosphate dehydrogenase deficiency

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glucose-6-phosphate dehydrogenase deficiency n. a hereditary (X-linked) condition in which absence of the enzyme glucose-6-phosphate dehydrogenase (G6PD), which functions in carbohydrate metabolism, results in haemolysis, usually after exposure to oxidants (such as drugs) or infections. See also favism.

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