Cutaneous lesions and visceral involvement of tuberous sclerosis: First report in North of Iran From: Journal of Pediatric Neurology | Date: January 1, 2007| Author: Juibary, Ali Ghabeli; Omran, Mohammadreza Salehi | Copyright Journal of Pediatric Neurology 2007. Provided by ProQuest LLC.Copyright information

Abstract.

Tuberous sclerosis (TS) is an autosomal dominant disorder with a significant range of clinical expressions. The involvement of vital organs, such as the brain, kidney, heart and lung is the main cause of death in patients with TS. The aim of this study is to summarize the characteristic cutaneous features and common extracutaneous involvement of TS, which are helpful to the early detection of visceral involvement. The analyzed clinical data from 10 patients with TS included t...

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